The human tooth is made up of four major tissues.  Enamel is the outer most layer of the tooth.  Because enamel is the outer most layer of the tooth it is open to dental problems, including genetic tooth disorders.  This article, brought to you by your 55110 dentist, White Bear Lake Dental, is going to look at the different genetic tooth enamel disorder types.


Dentinogenesis Imperfecta


Dentinogenesis imperfect is another genetic tooth disorder.  This disorder causes a normal enamel layer to flake off making teeth weak, prone to damage and sensitive.   Teeth are transparently discolored with this disorder.  They may turn unusual colors like blue-grey or yellow-brown.  lDentinogenesis imperfect affects both the primary and the secondary teeth.

There are three types of dentinogenesis imperfect:


Type 1 – inherited in autosomal recessive manner

Type 2  & Type 3  - inherited in autosomal dominant maner


48,XXYYY Syndrome


Affecting 1 in 18,000 males, this condition is another very rare condition.  While this syndrome interferes with sexual development it also causes common dental problems, such as thinned tooth enamel.  It also causes infertility, abnormal body growth and reduced height.


Oculodentodigital Dysplasia


One of the rarest genetic tooth enamel diseases, oculodentodigital dysplasia, affects less than 1, 000 people worldwide.  This disease affects eyes and fingers as well as the teeth.  Oculodentodigital dysplasia causes enamel to become weak making teeth higher at risk to tooth damage.


Amelogenesis Imperfecta


An Inherited tooth disorder, Amelogenesis imperfect, is when the enamel is abnormally formed and thin. Amelogenesis imperfect is inherited in autosomal dominant manner.  The mineralization of the enamel is affected.  It causes the teeth to become soft, thin and damage easily.  Because the enamel is thin the tooth color is usually yellow.


You should consult your dental professional about any of the above genetic tooth enamel tooth disorders that you would like more information on. It is important to know family dental history and to discuss genetic tooth enamel disorder types to prevent future dental complications.